Creutzfeldt-Jakob Disease

CJD-Surveillance System

Statistics

• Referrals of Suspected CJD Reported to CJD-SS
• CJD Cases Reported to CJD-SS
• CJD Cases Reported by Province
• Incidence of CJD Cases Reported to CJD-SS in Canada

Referrals of Suspected CJD Reported by CJD-SS¹,
1997-2009² as of September 30, 2009

Year of Reporting	Number of Referrals
1997	4
1998	43
1999	63
2000	82
2001	101
2002	103
2003	75
2004	90
2005	96
2006	78
2007	101
2008	100
2009	79
Total Referrals	1015

Notes:
¹CJD-SS began in April 1998
²Data before April 1998 are retrospective and partial, data from 1999 to 2007 are complete, and data for 2008 and 2009 are provisional

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CJD Deaths Reported by CJD-SS¹, 1994-2009² as of September 30, 2009

Deaths of Definite and Probable CJD
Year	Sporadic	Iatrogenic	Familial	GSS	FFI	vCJD	Total
1994	2	0	0	1	0	0	3
1995	3	0	0	0	0	0	3
1996	13	0	0	0	0	0	13
1997	16	0	1	1	0	0	18
1998	22	1	0	1	0	0	24
1999	26	2	2	1	0	0	31
2000	32	0	0	3	0	0	35
2001	27	0	2	1	0	0	30
2002	31	0	2	2	0	1	36
2003	27	1	1	0	0	0	29
2004	42	0	1	0	0	0	43
2005	42	0	0	2	0	0	44
2006	37	0	1	3	1	0	42
2007	32	0	0	3	0	0	35
2008	37	0	0	0	0	0	37
2009	9	0	0	0	0	0	9
Total	398	4	10	18	1	1	432

Notes:
¹CJD-SS began in April 1998
²Data before April 1998 are retrospective and partial, data from 1999 to 2007 are complete, and data for 2008 and 2009 are provisional
Final classification of 35 cases from 2007/08 is pending.

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CJD Cases by Province/Territory As of September 30, 2009

Incidence of CJD Deaths Reported by CJD-SS in Canada As of September 30, 2009

Year of Death	Total CJD Cases	Population of Canada	Incidence Rate
1999	31	30,403,878	1.02
2000	35	30,689,035	1.14
2001	30	31,021,251	0.97
2002¹	36	31,372,587	1.15
2003	29	31,669,150	0.92
2004	43	32,069,999	1.34
2005	42	32,378,122	1.30
2006	42	32,730,213	1.28
2007	34	33,091,228	1.03
2008²	37	33,223,840	1.11
2009²	9	33,311,420	0.27

World Wide average occurrence of CJD is approximately 1-2 per million population

Notes:
¹ As of September 2002, CJD cases include both definite and probable cases of CJD
²Data from 1999 to 2007 are complete, and data for 2008 and 2009 are provisional
2008 Population Source: http://www.statcan.ca/Daily/English/080625/d080625b.htm
Final classification of 35 cases from 2007/08 is pending.

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National Microbiology Laboratory Genetics and Prion Disease program (HGPD)