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Creutzfeldt-Jakob Disease

CJD-Surveillance System

Statistics


Data tables are also available in an alternate format for downloading or viewing:
Statistics: December 2015 PDF Version (773 KB - 4 pages)

Referrals of Suspected CJD Reported by CJDSS, 1997-2015
As of December 31, 2015
Year of Reporting Number of Referrals
1997 4
1998 43
1999 63
2000 82
2001 101
2002 103
2003 75
2004 90
2005 97
2006 80
2007 101
2008 100
2009 104
2010 76
2011 102
2012 103
2013 99
2014 99
2015 91
Total 1613
CJD Deaths Reported by CJDSS, 1994-2015
As of December 31, 2015
Deaths of Definite and Probable CJD
Year Sporadic Iatrogenic Familial GSS FFI vCJD Total
Cases with definite & probable diagnosis to date.
1994 2 0 0 1 0 0 3
1995 3 0 0 0 0 0 3
1996 13 0 0 0 0 0 13
1997 16 0 1 1 0 0 18
1998 22 1 0 1 0 0 24
1999 27 2 2 1 0 0 32
2000 32 0 0 3 0 0 35
2001 27 0 2 1 0 0 30
2002 31 0 2 2 0 1 36
2003 27 1 1 0 0 0 29
2004 42 0 1 1 0 0 44
2005 42 0 1 1 0 0 44
2006 39 0 1 3 1 0 44
2007 35 0 0 4 0 0 39
2008 48 0 1 0 0 0 49
2009 48 0 3 2 0 0 53
2010 35 0 3 0 0 0 38
2011 46 0 3 1 0 1 51
2012 62 0 1 0 0 0 63
2013 50 0 0 0 1 0 51
2014 50 0 4 0 1 0 55
2015 29 0 2 1 2 0 34
Total 726 4 28 23 5 2 788

CJD Cases by Province/Territory December 31, 2015

Text Equivalent - CJD Cases by Province/Territory December 31, 2015

Incidence of CJD Deaths Reported by CJDSS in Canada
As of December 31, 2015
Year of Death Total CJD Cases Population of Canada Incidence Rate
Cases with definite & probable diagnosis to date.
2014 Population SourceExternal Link
1999 32 30,492,106 1.05
2000 35 30,783,969 1.14
2001 30 31,130,030 0.96
2002 36 31,450,443 1.14
2003 29 31,734,851 0.91
2004 44 32,037,434 1.37
2005 44 32,352,233 1.36
2006 44 32,678,986 1.35
2007 39 33,001,076 1.18
2008 49 33,371,810 1.47
2009 53 33,756,714 1.57
2010 38 34,131,451 1.11
2011 51 34,472,304 1.48
2012 63 34,880,248 1.81
2013 51 35,289,003 1.45
2014 55 35,675,834 1.54
2015 34 35,702,707 0.95

World Wide average occurrence of CJD is approximately 1-2 per million population

European Creutzfeldt Jakob Disease Surveillance NetworkExternal Link