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Creutzfeldt-Jakob Disease

CJD-Surveillance System

Statistics


Data tables are also available in an alternate format for downloading or viewing:
Statistics August 2014 PDF Version (539 KB - 4 pages)

Referrals of Suspected CJD Reported by CJDSSReferrals - Footnote 1, 1997-2014Referrals - Footnote 2
As of August 31, 2014
Year of Reporting Number of Referrals
Referrals - Footnote 1
CJDSS began in 1998
Referrals - Footnote 2
Data before 1998 are retrospective and partial, data from 1999 to 2013 are complete, and data for 2014 is provisional
1997 4
1998 43
1999 63
2000 82
2001 101
2002 103
2003 75
2004 90
2005 97
2006 80
2007 101
2008 100
2009 104
2010 76
2011 102
2012 103
2013 99
2014 61
Total 1484

CJD Deaths Reported by CJDSSDeaths Reported - Footnote 1, 1994-2014Deaths Reported - Footnote 2
As of August 31, 2014

Deaths of Definite and Probable CJD
Year Sporadic Iatrogenic Familial GSS FFI vCJD Total
Deaths Reported - Footnote 1
CJDSS began in 1998
Deaths Reported - Footnote 2
Data before 1998 are retrospective and partial, data from 1998 to 2012 are complete, and data for 2013 - 2014 are provisional
1994 2 0 0 1 0 0 3
1995 3 0 0 0 0 0 3
1996 13 0 0 0 0 0 13
1997 16 0 1 1 0 0 18
1998 22 1 0 1 0 0 24
1999 27 2 2 1 0 0 32
2000 32 0 0 3 0 0 35
2001 27 0 2 1 0 0 30
2002 31 0 2 2 0 1 36
2003 27 1 1 0 0 0 29
2004 42 0 1 1 0 0 44
2005 42 0 1 1 0 0 44
2006 39 0 1 3 1 0 44
2007 35 0 0 4 0 0 39
2008 48 0 1 0 0 0 49
2009 48 0 3 2 0 0 53
2010 35 0 3 0 0 0 38
2011 46 0 3 1 0 1 51
2012 61 0 1 0 0 0 62
2013 43 0 0 0 1 0 44
2014 14 0 2 0 0 0 16
Total 653 4 24 22 2 2 707

CJD Cases by Province/Territory August 31, 2014CJD Cases by Province/Territory August 31, 2014

Text Equivalent - CJD Cases by Province/Territory August 31, 2014

Incidence of CJDFootnote 1 Deaths Reported by CJDSS in Canada
As of August 31, 2014
Year of Death Total CJD Cases Population of Canada Incidence Rate
Table 3 - Footnote 1
As of September 2002, CJD cases include both definite and probable cases of CJD
Table 3 - Footnote 2
Data from 1998 to 2012 are complete, and data for 2013 - 2014 are provisional
Table 3 - Footnote
Population Source: Statistics Canada, Demography Division
1999 32 30,401,286 1.05
2000 35 30,685,730 1.14
2001 30 31,019,020 0.97
2002Incidence of CJD - Footnote 1 36 31,353,656 1.15
2003 29 31,639,670 0.92
2004 44 31,940,676 1.38
2005 44 32,245,209 1.36
2006 44 32,576,074 1.35
2007 39 32,931,956 1.18
2008 49 33,327,337 1.47
2009 53 33,739,814 1.57
2010 38 33,841,500 1.12
2011 51 34,019,075 1.50
2012 62 34,482,779 1.80
2013Incidence of CJD - Footnote 2 44 35,158,304 1.25
2014Incidence of CJD - Footnote 2 16 35,295,770 0.68

World Wide average occurrence of CJD is approximately 1-2 per million population

European Creutzfeldt Jakob Disease Surveillance NetworkExternal Link